ea0029p342 | Clinical case reports - Pituitary/Adrenal | ICEECE2012
Franco M.
, Alencar G.
, Faria A.
, Bezerra J.
, Cruz C.
, Domenice S.
, Lima L.
, Lerario A.
, Almeida M.
, Latronico A.
, Mendonca B.
, Fragoso M.
Introduction: Adrenocortical carcinoma (ACC) is a rare and potentially fatal disease in childhood. Complete resection of the tumor and metastasis can improve survival. Case: A 2.6 year-old boy presented isosexual pseudo-precocious puberty at 2.1 years. CT revealed a single nodule in the left adrenal (2 cm) which was resected by adrenalectomy. Histology revealed an adrenocortical tumor (2 cm, 3.0 g, Weiss score 4), ENSAT stage I. Partial regression of the puberty features and n...